Interstitial Lung Disease in Children With Selected Primary Immunodeficiency Disorders—A Multicenter Observational Study
نویسندگان
چکیده
منابع مشابه
Sjögren's syndrome-associated interstitial lung disease: A multicenter study.
UNLABELLED Primary Sjögren syndrome (PSS) is a chronic inflammatory autoimmune disease. Interstitial lung disease (ILD) can be an extraglandular complication. OBJECTIVE To evaluate the clinical characteristics of patients diagnosed with PSS with ILD. METHODS Multicentre cohort study with 25 patients diagnosed with PSS and ILD. Data of PSS, prognostic factors, pulmonary involvement variables...
متن کاملInterstitial lung disease in children.
PURPOSE OF REVIEW In this review, we discuss the recent advances in our understanding of the cause, pathogenesis, presentation, diagnosis, treatment, and prognosis of interstitial lung disease (ILD) in children. RECENT FINDINGS The classification of ILD syndromes in children greater than 2 years of age is based largely on adult classification schemes. In children less than 2 years of age, cla...
متن کاملChronic interstitial lung disease in children.
Children's interstitial lung diseases (chILD) are increasingly recognised and contain many lung developmental and genetic disorders not yet identified in adult pneumology. Worldwide, several registers have been established. The Australasian Registry Network for Orphan Lung Disease (ARNOLD) has identified problems in estimating rare disease prevalence; focusing on chILD in immunocompetent patien...
متن کاملChronic interstitial lung disease in children
Métodos: Estudo retrospectivo de 25 pacientes imunocompetentes, de 2 meses a 17 anos, com doença pulmonar intersticial crônica, internados no Setor de Pneumologia, Serviço de Pediatria do Hospital dos ServidoresdoEstado, porumperíodode20anos (1984-2004).Seguiu-se protocolo para pneumopatias crônicas persistentes e selecionaram-se os casos de doença intersticial. Foram avaliados aspectos clínico...
متن کامل[Interstitial lung disease in patients with primary biliary cirrhosis].
Primary biliary cirrhosis (PBC) is a chronic autoimmune disorder of unknown etiology. The disease affects middle-aged women and is characterized by the destruction of the intralobular bile ducts that causes consequent cholestasis. AMA is a hallmark of PBC, composed mostly of IgG and IgM class. The M2 antibody is the most specific one, with sensitivity range of 54-98% depending on type of tes...
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ژورنال
عنوان ژورنال: Frontiers in Immunology
سال: 2020
ISSN: 1664-3224
DOI: 10.3389/fimmu.2020.01950